{"id":276,"date":"2025-10-07T01:19:07","date_gmt":"2025-10-06T16:19:07","guid":{"rendered":"https:\/\/kashiwa-gomi-shikanaika.com\/blog\/?p=276"},"modified":"2025-12-22T13:24:44","modified_gmt":"2025-12-22T04:24:44","slug":"post-276","status":"publish","type":"post","link":"https:\/\/kashiwa-gomi-shikanaika.com\/blog\/post-276\/","title":{"rendered":"Erdheim\u2013Chester disease\uff1a\u30a8\u30eb\u30c8\u30cf\u30a4\u30e0\u30fb\u30c1\u30a7\u30b9\u30bf\u30fc\u75c5\uff08\u814e\u5468\u56f2\u306b\u8a8d\u3081\u305f\u975e\u30e9\u30f3\u30b2\u30eb\u30cf\u30f3\u30b9\u7d30\u80de\u7d44\u7e54\u7403\u75c7\uff09"},"content":{"rendered":"\n

62\u6b73\u7537\u6027\u3002\u80c6\u77f3\u306e\u8a55\u4fa1\u3092\u53d7\u3051\u308b\u305f\u3081AUS\u65bd\u884c\u3055\u308c\u305f\u3068\u3053\u308d\u5f8c\u8179\u819c\u306b\u816b\u7624\u304c\u3042\u308b\u3053\u3068\u304c\u6307\u6458\u3055\u308c\u5185\u79d1\u5916\u6765\u7d39\u4ecb\u53d7\u8a3a\u3002<\/p>\n\n\n\n

\u30d0\u30a4\u30bf\u30eb\u30b5\u30a4\u30f3\u306f\u6b63\u5e38\u3067\u3001\u8eab\u4f53\u691c\u67fb\u306b\u304a\u3044\u3066\u3082\u7279\u8a18\u3059\u3079\u304d\u7570\u5e38\u3092\u8a8d\u3081\u306a\u304b\u3063\u305f\u3002<\/p>\n\n\n\n

\u63a1\u8840\u6240\u898b\u3067\u306f\u814e\u6a5f\u80fd\u6b63\u5e38\u3002<\/p>\n\n\n\n

CT\u6240\u898b\u3067\u306f\u814e\u81d3\u5468\u56f2\u306e\u8edf\u7d44\u7e54\u3001\u4e21\u5074\u91cd\u5ea6\u306e\u6c34\u814e\u75c7\u304c\u793a\u3055\u308c\u305f\u3002<\/p>\n\n\n\n

\"\"<\/figure>\n\n\n\n

\u305d\u306e\u5f8cPET-CT\u3082\u64ae\u5f71\u3055\u308c\u305f\u304c\u3001\u7570\u5e38\u96c6\u7a4d\u90e8\u4f4d\u306f\u8a8d\u3081\u306a\u304b\u3063\u305f\u3002<\/p>\n\n\n\n

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\"\"<\/figure>\n\n\n\n

\u514d\u75ab\u67d3\u8272\u306b\u3088\u308a\u7d30\u80de\u306fCD68\u5f37\u967d\u6027\u3001S100\u3001CD1a\u9670\u6027\u3060\u3063\u305f\u3002BRAF V600E\u5909\u7570\u306f\u967d\u6027\u3060\u3063\u305f\u3002<\/p>\n\n\n\n

\u4ee5\u4e0a\u304b\u3089\u300cErdheim\u2013Chester disease\uff1a\u30a8\u30eb\u30c8\u30cf\u30a4\u30e0\u30fb\u30c1\u30a7\u30b9\u30bf\u30fc\u75c5\u300d\u3068\u8a3a\u65ad\u3055\u308c\u305f\u3002<\/p>\n\n\n\n

\u30a8\u30eb\u30c8\u30cf\u30a4\u30e0\u30fb\u30c1\u30a7\u30b9\u30bf\u30fc\u75c5\u306f\u975e\u30e9\u30f3\u30b2\u30eb\u30cf\u30f3\u30b9\u7d30\u80de\u7d44\u7e54\u7403\u75c7\u3067\u3042\u308a\u3001\u901a\u5e38\u9577\u9aa8\u306e\u786c\u5316\u6027\u75c5\u5909\u3068\u3057\u3066\u73fe\u308c\u308b\u3002<\/p>\n\n\n\n

\u3053\u306e\u75be\u60a3\u306f\u5f8c\u8179\u819c\u814e\u5468\u56f2\u7d44\u7e54\u306e\u6d78\u6f64\u3092\u542b\u3080\u591a\u304f\u306e\u9aa8\u5916\u6240\u898b\u3068\u3082\u95a2\u9023\u3057\u3066\u304a\u308a\u3001\u814e\u81d3\u5468\u56f2\u306e\u6240\u898b\u306f\u300c\u6bdb\u6df1\u3044\u814e\u81d3\u300d\u3068\u547c\u3070\u308c\u3066\u7279\u5fb4\u7684\u753b\u50cf\u3092\u793a\u3059\u3002<\/p>\n\n\n\n

\u6cbb\u7642\u3068\u3057\u3066\u306f\u5909\u7570\u578bBRAF V600E\u30ad\u30ca\u30fc\u30bc\u306e\u6a19\u7684\u963b\u5bb3\u85ac\uff08\u30d9\u30e0\u30e9\u30d5\u30a7\u30cb\u30d6\uff09\u306b\u3088\u308b\u6cbb\u7642\u304c\u958b\u59cb\u3055\u308c\u305f\u3002<\/p>\n\n\n\n

1\u5e74\u5f8c\u306e\u30d5\u30a9\u30ed\u30fc\u3067\u306f\u75c5\u6c17\u306e\u9032\u884c\u306f\u898b\u3089\u308c\u3066\u3044\u306a\u3044\u3002<\/p>\n\n\n\n

\n

N Engl J Med 2023; 388:925<\/p>\n\n\n\n

DOI: 10.1056\/NEJMicm2208776<\/p>\n<\/blockquote>\n","protected":false},"excerpt":{"rendered":"

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